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A total of 434 tumors of the peripheral nerve and neuroectodermal tissue is hiatologically analyzed. These tumors were collected from Department of Pathology, Seoul National University, during a period of 17 years from January 1963 to December 1979, After critical review of the diagnosis of tumars and their clinical data we have obtained following informations. l. Among 434 tumors in this series there were 174 cases of neurilemmoma, 72 cases of solitary benign neurofibroma, 128 cases of neurofibromatosis, 25 cases of neurogenic sarcama (malignant schwannorna), 29 cases of neuroblastoma, 4 cases ot ganglio- neuroblaatoms and 2 cases of ganglioneuroma. 2. Neurilemmoma was found more frequently in sofc tissue(61%) and spinal canal(25%), and the remainder occured in cranial cavity. The average age was 39.7 years and sex ratio was I: 1.1. 3. Seventy two cases of. solitary benign neurofibroma occurred mostly in soft tissue(93%). The remaining fivc cases occurred in spinal canal. Among soft tisaue tumors, head and neck were the sites in 23 cases, trunk in 23 cases and extremities in 21 cases. In 9 cases we could identify the nerve trunk from whicb the tumar arose. Among these cases sciatic nerve was the most common. 4. Neurafibromatosis was usually characterized by plexiform pattern of the tumors. However, cutaneous involvement did not show charactersitic plexifrom structure. In this series there was not a aingle case of malignant transformatian among 12S neurofi- bromatosis. 5. There were 25 cases of malignant schwannoma. Among those 23 cases occurred in soft tissue and the remaining two cases accurred in the spinal canal. The site distributioa of soft tissue neurogenic sarcomas was 13 in trunk, 6 in extremities, and 4 in head and neck. 6. Twenty-nine neuroblastomas occurred most frequently in adrenals and retroperitoneum(86%). The remainder occurred in mediastinem(2 cases), nasal cavity(1 case) and spinal(1 case). average age of neuroblastomas was 8.6 years and sex ratio was 1.9:1.
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